Small round cell mesenchymal tumors

Polyphenotypic small round cell tumor (DSMCT) Mesenchymal chondrosarcoma... 

Few mesenchymal tumors including desmoplastic small round cell tumor, leiomyosarcoma and monophasic synovial sarcoma. 

T-cell lymphoma, ALCL, AML, GIST, breast metaplastic carcinoma, ovarian sex cord stromal tumors, synovial sarcoma, Merkel cell carcinoma, endocrine and neuroendocrine tumors, desmoplastic small round cell tumor, melanoma, nephroblastoma, ependymoma, mesenchymal chondrosarcoma, extrarenal malignant rhabdoid tumor, rhabdomyosarcoma, meningeal... 

Wilms tumor Triphasic blastemal, epithelial, and stromal components. Blastemal cells small, round or oval, in nodules or serpentine patterns. Epithelial component primitive rosette-like to tubular or papillary. Mesenchymal component fibrous, myoid, adipose, chondroid, osseous, neural. Blastemal vimentin, desmin. Epithelial cytokeratin. Mesenchymal variable according to differentiation pattern. Various abnormalities including mutations of WT1 at 11 pi 3 and WT2 at 11 pi 5 numeric and structural karyotypic abnormalities of chromosomes 1, 11, 13, 14, 16, 1 7, 19, and 22. 

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