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N-Acetylgalactosamine-6-sulfatase

Arylsulfatase B (N-acetylgalactosamine 4-sulfatase) is a deficient enzyme in patients witti the genetic defect disease MPS VI. Like MPS I, GAGs are only partially broken down, and carbohydrate residues build relentlessly in the lysosomesof cells. Also like a-L-iduroni-dase replacement, the exogenous supply of arylsulfatase could breakdown the stored GAGs and cellular function could be restored. [Pg.219]

Harmatz P, et al (2005). Direct comparison of measures of endurance, mobility, and joint function during enzyme-replacement therapy of mucopolysaccharidosis VI (Maro-teaux-Lamy syndrome) Results after 48 weeks in a phase 2 open-label clinical study of recombinant human N-acetylgalactosamine 4-sulfatase. Pediatr. 115(6) e681-e689. [Pg.735]

Table 18,9, N-Acetylgalactosamine 4-sulfatase Maroteaux-Lamy syndromCj MPS VI) ... Table 18,9, N-Acetylgalactosamine 4-sulfatase Maroteaux-Lamy syndromCj MPS VI) ...
VI Maroteaux-Lamy (mild or severe) 253200 Dermatan sulfate N-acetylgalactosamine- 5ql2 4-sulfatase... [Pg.380]

See other pages where N-Acetylgalactosamine-6-sulfatase is mentioned: [Pg.485]    [Pg.251]    [Pg.394]    [Pg.788]    [Pg.190]    [Pg.724]    [Pg.728]    [Pg.677]    [Pg.485]    [Pg.251]    [Pg.394]    [Pg.788]    [Pg.190]    [Pg.724]    [Pg.728]    [Pg.677]    [Pg.315]   
See also in sourсe #XX -- [ Pg.346 ]

See also in sourсe #XX -- [ Pg.380 , Pg.391 ]



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