SEARCH Articles Figures Tables 3 -Hydroxy-3 -methylglutaryl 3- Hydroxy-3-methylglutaryl CoA lyase deficiency 3- Hydroxy-3-methylglutaryl-CoA (HMG 3-Hydroxy-3-methylglutaryl-CoA lyase 3-Hydroxy-3-methylglutaryl-CoA synthase (HMG 3-Hydroxy-3-methylglutaryl-CoA synthesis 3-Hydroxy-3-methylglutaryl-CoA synthetase 3-methylglutaryl Hydroxy methylglutaryl-CoA reductase Hydroxy-3-methylglutaryl-CoA synthetase (EC S-3-Hydroxy-3-methylglutaryl-CoA