Fatty acid /?-oxidation and ketogenesis

Inherited CPT-I deficiency affects only the fiver, resulting in reduced fatty acid oxidation and ketogenesis, witfi fiypoglycemia. CPT-II deficiency affects pri-... [Pg.187]

Auestad, N., Korsak, R. A., Morrow, J. W. etal. Fatty acid oxidation and ketogenesis by astrocytes in primary culture. /. Neurochem. 56 1376-1386,1991. [Pg.555]

McGarry, J. D., Mannaerts, G. P., and Foster, D. W. 1977. A possible role for malonyl-CoA in the regulation of hepatic fatty acid oxidation and ketogenesis. J. Clin. Invest. 60 265-270. [Pg.392]

Clinical problems related to fatty acid metabolism. Deficiencies in carnitine lead to an inability to transport fatty acids into the mitochondria for oxidation. This can occur in newborns and particularly in pre-term infants. Treatment is by oral carnitine administration. Carnitine palmitoyltransferase I (CPT I) deficiency primarily affects the liver and leads to reduced fatty acid oxidation and ketogenesis. CPT II deficiency results in recurrent muscle pain, fatigue and myoglobinuria following strenuous exercise. [Pg.41]

Current Views of Fatty Acid Oxidation and Ketogenesis From Organelles to Point Mutations edited by Quant and Eaton, Kluwer Academic / Plenum Pubhsheis, New York, 1999. 1... [Pg.3]

Fatty Acid Oxidation and Ketogenesis in Rat Liver under Proliferation of Mitochondria and Peroxisomes... [Pg.125]

Big Chemical Encyclopedia

Chemical substances, components, reactions, process design ...