Compound 20, from Morquio syndrome type

Compound 20 is a reducing oligosaccharide consisting of the man-notriose branching core bearing an N-acetyllactosamine unit in the lower branch 20 was obtained as the main component of a mixture also containing 19. As already described, this mixture has been isolated from the urine of a patient suffering84,65 from Morquio syndrome type B. The 500-MHz, H-n.m.r. spectrum of the mixture is depicted in Fig. 19 the relevant, spectral parameters for 20 are compiled in Table VIII. 

Compound 11 has been isolated from the urine of patients suffering from GM,-gangliosidosis52 64,643 or from64 65 Morquio syndrome type B. This reducing decasaccharide is isomeric with oligosaccharide 10. It contains three N-acetyllactosamine units, the third unit being attached to 0-6 of Man-4. This structure is denoted as a tri -antennary oligosaccharide. 

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