Benign familial recurrent cholestasis

Familial diseases include Dubin-Johnson syndrome, Rotor s syndrome, and benign familial recurrent cholestasis. Serum bilirubin values in Dubin-Johnson syndrome are the same as those found in Rotor s syndrome (Table 29-2). Very little is known about benign familial recurrent cholestasis. All three disorders are uncommon or rare, and all are benign. The liver in Dubin-Johnson... 

ATP8B1 NBD-PS, PS , PE Progressive familial intrahepatic cholestasis, benign recurrent intrahepatic cholestasis... 

G. F. de Pagter, Familial and nonfamilial benign recurrent cholestasis distinguished by plasma disappearance of indocyanine green but not cholyglycerine. Gut, 19 345 (1978). 

Huinink and K. H. Brandt, Familial benign recurrent intrahepatic cholestasis Interrelation with intrahepatic cholestasis of pregnancy and from oral contraceptives, Gastroenterol., 71 202 (1976). 

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