Storage pool deficiency, dense granule

Dense granule storage pool deficiency Deficiency of dense granules in megakaryocytes and platelets... 

Lages B, Holmsen H, Weiss HJ, Dangelmaier C. 1983. Thrombin and ionophore A23187-induced dense granule secretion in storage pool deficient platelets Evidence for impaired nucleotide storage as the primary dense granule defect Blood 61 154-162. 

Patients with storage pool deficiency who are selectively deficient in dense granules produce smaller thrombi in perfusion studies [4], though some patients may also present an adhesion defect probably related to reduced ADP release [60]. 

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