Nutrition for patients with genetic disorders

Patients snffering from metabolic disorders such as phenylketonuria (PKU), branched-chain ketoaciduria (maple syrup urine disease, MSUD), nrea and ammonia disorders or glycogen storage disease reqnire formulations manufactured specifically for each disease (Elsas Acosta, 2006). (Appendix 15.1). 

A problem with vegan diets is whether they can provide snfficient protein and some micronntrients. Foods recommended are whole grains and grain prodncts e.g. wheat, millet, barley, rice, rye, oats, maize, wholemeal breads and pastas) pulses and products made from them (e.g. peas, beans, lentils, tofu) fresh vegetables (including green leafy vegetables and salads) fresh and dried fruits nuts seeds (e.g. sunflower, sesame and pumpkin). 

Vegetables should be cooked as lightly as possible, and the cooking water (which contains minerals and vitamins) used in soups and stocks. Salads and raw vegetables are particnlarly good sources of vitamins and minerals. Seeds are more nutritious if they are ground or milled. Dried frnits are good sources of some minerals. 

Two miCTonutrients of particular concern in vegan diets are vitamin B,2 and iron which are normally obtained from meat. A dietary supply of vitamin B,2 can be ensured from sources such as yeast extracts or soya protein. 

Plant foods Diseases in which risk is decreased Mechanism by which risk is decreased 

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