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HEMPAS Hereditary Erythroblastic Multinuclearity with Positive Acidified Serum

Fukuda MN. HEMPAS. Hereditary erythroblastic multinuclearity with positive acidified serum lysis test. Biochim Biophys Acta 1999 1455 231-239. [Pg.306]

Congenital dyserythropoietic anemia (CDA) is a group of inherited disorders characterized by an ineffective erythropoiesis, bone marrow erythroid multinuclearity, and secondary tissue siderosis. In 1968, Heimpel and Wendt classified CDA into three types [18]. CDA type II is the most common CDA, and is also called HEMPAS, since Crookston characterized this disease as Hereditary Erythroblastic Multinuclearity with Positive Acidified Serum lysis test [19]. [Pg.2055]

HEMPAS hereditary erythroblastic multinuclearity with a positive acidified-serum-lysis test (congenital dyserythropoietic anemia type II)... [Pg.4]


See other pages where HEMPAS Hereditary Erythroblastic Multinuclearity with Positive Acidified Serum is mentioned: [Pg.231]    [Pg.2051]    [Pg.231]    [Pg.2051]   


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Hereditary erythroblastic multinuclearity HEMPAS)

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