Fructosuria Fructokinase

Essential fructosuria is a benign, asymptomatic condition arising from deficiency of the enzyme fructokinase that causes a portion of fructose to be excreted in the urine. 

DHAP is a glycolysis intermediate, whereas glyceraldehyde must be reduced by a mitochondrial enzyme, glyceraldehyde dehydrogenase, to glycerol, which is then subject to action by glycerol kinase in the liver. The aldolase seems to be the principal pathway of metabolizing fructose and depends on the initial phosphorylation step catalyzed by fructokinase, which produces fructose-l-phosphate. Fructokinase is defective in an inherited disorder, essential fructosuria. Fructose-l-phosphate aldolase is deficient in the hereditary disorder fructose intolerance. 

Fructokinase is deficient in essential fructosuria therefore, fructose can-s not be metabolized as rapidly as it normally would. Blood fructose levels... 

Essential fructosuria A rare, benign genetic condition in which fructose spills over to the urine because the Uver, kidney, and intestine lack the enzyme fructokinase. 

There are two genetic diseases associated with fructose metabolism. One is fructosuria, in which the liver enzyme, fructokinase, is missing. Thus, fructose is not metabolized but, instead, accumulates in the blood and is passed into... 

Essential fructosuria which is a benign condition caused by a deficiency of the enzyme fructokinase. 

Essential fructosuria is an unrelated and completely harmless condition caused by deficiency of fructokinase [32]. 

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