What Is Isobutyryl-CoA Dehydrogenase Deficiency

Isobutyryl-coenzyme A (CoA) dehydrogenase deficiency (IBD deficiency) is a rare disorder in which the body is unable to process certain proteins properly. People with this disorder have inadequate levels of an enzyme that helps break down the amino acid valine, a building block of proteins. 

2 This section has been adapted from the National Library of Medicine http //ghr.nlm.nih.gov/. 

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