Transmissible spongiform species

Not listed in Box 25.2 is the zoonosis arising from bovine spongiform encephalopathy (BSE), or mad cow disease . There is no conclusive evidence that the transmissible spongiform encephalopathies of man are acquired from animals, but the occmrence of so-called new variant Creutzfeld Jakob disease in man that has coincided with an epidemic of mad cow disease in cattle and related species has led to the... 

Bruce, M. etal. Transmission of bovine spongiform encephalopathy and scrapie to mice Strain variation and the species barrier. Philos. Trans. R. Soc. Bond. [Biol] 343 405-411, 1994. 

Creutzfeldt-Jakob disease (CJD), Gerstmann-Straussler-Scheinker syndrome, fatal familial insomnia, and kuru are fatal diseases of the central nervous system, known as transmissible subacute spongiform encephalopathies (193). Creutzfeldt-Jakob disease is the most common of these and has an incidence of 1 1000 000 in most countries. About 10% of those involved have a familial disposition, but most cases occur sporadically. There are similar diseases in sheep (scrapie), cattle (bovine spongiform encephalopathy), and other animal species. The cause of the... 

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