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2-Oxoadipate dehydrogenase

If the outlined metabolic pathway is correct, 2-aminoadipic aciduria without or with minimal 2-oxoadipic aciduria could result from a defect in mitochondrial 2-aminoadipate aminotransferase deficiency with 2-oxoadi-pic aciduria only originating from tryptophan. A defect in 2-oxoadipate dehydrogenase would be the cause of 2-oxoadipic aciduria [6]. [Pg.278]

Table 12.3a+b. 2-Aminoadipate aminotransferase/2-oxoadipate dehydrogenase ia) (13 patients known) deficiency (2-amino/2- oxoadipic acidur-... [Pg.284]

See other pages where 2-Oxoadipate dehydrogenase is mentioned: [Pg.278]    [Pg.279]    [Pg.685]    [Pg.278]    [Pg.279]    [Pg.685]    [Pg.639]    [Pg.1386]    [Pg.473]    [Pg.452]    [Pg.477]    [Pg.341]    [Pg.342]   
See also in sourсe #XX -- [ Pg.281 ]



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