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Non-ketotic dicarboxylic aciduria,

Twin English siblings with non-ketotic dicarboxylic aciduria, features of Reye s syndrome and with close similarities to Jamaican vomiting sickness (organic aciduria, hypoglycaemia, diarrhoea and vomiting, acidosis without ketosis)... [Pg.369]

Table 14.6 Concentrations of urinary organic acids (extracted by DEAE-Sephadex) in twin English siblings with non-ketotic dicarboxylic aciduria (after Chalmers et al, 1980). [Pg.373]




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